Treatment effect of coenzyme Q 10 and an antioxidant cocktail in fibroblasts of patients with Sanfil...
Treatment effect of coenzyme Q 10 and an antioxidant cocktail in fibroblasts of patients with Sanfilippo disease
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Language
English
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Coenzyme Q
10
(CoQ
10
) plays a key role in the exchange of electrons in lysosomal membrane, which contributes to protons’ translocation into the lumen and to the acidification of intra‐lysosomal medium, which is essential for the proteolytic function of hydrolases responsible ‐when deficient‐ of a wide range of inherited lysosomal dise...
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Full title
Treatment effect of coenzyme Q 10 and an antioxidant cocktail in fibroblasts of patients with Sanfilippo disease
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TN_cdi_crossref_primary_10_1007_s10545_013_9668_1
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https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_crossref_primary_10_1007_s10545_013_9668_1
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ISSN
0141-8955
E-ISSN
1573-2665
DOI
10.1007/s10545-013-9668-1
