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Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B

Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_0de39a40d2af49bb9bb31819d111a9f9

Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B

About this item

Full title

Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B

Publisher

London: Nature Publishing Group UK

Journal title

Nature communications, 2019-06, Vol.10 (1), p.2430-13, Article 2430

Language

English

Formats

Publication information

Publisher

London: Nature Publishing Group UK

More information

Scope and Contents

Contents

Muscle loss due to fibrotic or adipogenic replacement of myofibers is common in muscle diseases and muscle-resident fibro/adipogenic precursors (FAPs) are implicated in this process. While FAP-mediated muscle fibrosis is widely studied in muscle diseases, the role of FAPs in adipogenic muscle loss is not well understood. Adipogenic muscle loss is a...

Alternative Titles

Full title

Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_doaj_primary_oai_doaj_org_article_0de39a40d2af49bb9bb31819d111a9f9

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_0de39a40d2af49bb9bb31819d111a9f9

Other Identifiers

ISSN

2041-1723

E-ISSN

2041-1723

DOI

10.1038/s41467-019-10438-z

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