A novel DSP zebrafish model reveals training- and drug-induced modulation of arrhythmogenic cardiomy...
A novel DSP zebrafish model reveals training- and drug-induced modulation of arrhythmogenic cardiomyopathy phenotypes
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Author / Creator
Celeghin, Rudy , Risato, Giovanni , Beffagna, Giorgia , Cason, Marco , Bueno Marinas, Maria , Della Barbera, Mila , Facchinello, Nicola , Giuliodori, Alice , Brañas Casas, Raquel , Caichiolo, Micol , Vettori, Andrea , Grisan, Enrico , Rizzo, Stefania , Dalla Valle, Luisa , Argenton, Francesco , Thiene, Gaetano , Tiso, Natascia , Pilichou, Kalliopi and Basso, Cristina
Publisher
London: Nature Publishing Group UK
Journal title
Language
English
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Publication information
Publisher
London: Nature Publishing Group UK
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More information
Scope and Contents
Contents
Arrhythmogenic cardiomyopathy (AC) is an inherited disorder characterized by progressive loss of the ventricular myocardium causing life-threatening ventricular arrhythmias, syncope and sudden cardiac death in young and athletes. About 40% of AC cases carry one or more mutations in genes encoding for desmosomal proteins, including Desmoplakin (Dsp)...
Alternative Titles
Full title
A novel DSP zebrafish model reveals training- and drug-induced modulation of arrhythmogenic cardiomyopathy phenotypes
Authors, Artists and Contributors
Author / Creator
Risato, Giovanni
Beffagna, Giorgia
Cason, Marco
Bueno Marinas, Maria
Della Barbera, Mila
Facchinello, Nicola
Giuliodori, Alice
Brañas Casas, Raquel
Caichiolo, Micol
Vettori, Andrea
Grisan, Enrico
Rizzo, Stefania
Dalla Valle, Luisa
Argenton, Francesco
Thiene, Gaetano
Tiso, Natascia
Pilichou, Kalliopi
Basso, Cristina
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Primary Identifiers
Record Identifier
TN_cdi_doaj_primary_oai_doaj_org_article_19472e78aa4e4bbcaaac30f07520d4e5
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_19472e78aa4e4bbcaaac30f07520d4e5
Other Identifiers
ISSN
2058-7716
E-ISSN
2058-7716
DOI
10.1038/s41420-023-01741-2