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Function of Ltbp-4L and fibulin-4 in survival and elastogenesis in mice

Function of Ltbp-4L and fibulin-4 in survival and elastogenesis in mice

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_57e40f79a57649e39df7b3cfe04bce2c

Function of Ltbp-4L and fibulin-4 in survival and elastogenesis in mice

About this item

Full title

Function of Ltbp-4L and fibulin-4 in survival and elastogenesis in mice

Publisher

England: The Company of Biologists Ltd

Journal title

Disease models & mechanisms, 2016-11, Vol.9 (11), p.1367-1374

Language

English

Formats

Publication information

Publisher

England: The Company of Biologists Ltd

More information

Scope and Contents

Contents

LTBP-4L and LTBP-4S are two isoforms of the extracellular matrix protein latent-transforming growth factor beta-binding protein 4 (LTBP-4). The mutational inactivation of both isoforms causes autosomal recessive cutis laxa type 1C (ARCL1C) in humans and an ARCL1C-like phenotype in Ltbp4
mice, both characterized by high postnatal mortality and se...

Alternative Titles

Full title

Function of Ltbp-4L and fibulin-4 in survival and elastogenesis in mice

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_doaj_primary_oai_doaj_org_article_57e40f79a57649e39df7b3cfe04bce2c

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_57e40f79a57649e39df7b3cfe04bce2c

Other Identifiers

ISSN

1754-8403

E-ISSN

1754-8411

DOI

10.1242/dmm.026005

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