BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling
BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling
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London: Nature Publishing Group UK
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English
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London: Nature Publishing Group UK
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Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disorder presenting with progressive heterotopic ossification (HO) in soft tissues. Early-stage FOP is characterized by recurrent episodes of painful tissue swelling (flare-ups), with numerous proliferation-activated mesenchymal stromal cells (MSCs) subsequently causing HO. However, the...
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BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling
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TN_cdi_doaj_primary_oai_doaj_org_article_738410d855c94041bf945288a48a8c04
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https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_738410d855c94041bf945288a48a8c04
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1757-4684,1757-4676
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1757-4684
DOI
10.1038/s44321-024-00174-3