Log in to save to my catalogue

BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling

BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_738410d855c94041bf945288a48a8c04

BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling

About this item

Full title

BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling

Publisher

London: Nature Publishing Group UK

Journal title

EMBO molecular medicine, 2025-01, Vol.17 (1), p.112-128

Language

English

Formats

Publication information

Publisher

London: Nature Publishing Group UK

More information

Scope and Contents

Contents

Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disorder presenting with progressive heterotopic ossification (HO) in soft tissues. Early-stage FOP is characterized by recurrent episodes of painful tissue swelling (flare-ups), with numerous proliferation-activated mesenchymal stromal cells (MSCs) subsequently causing HO. However, the...

Alternative Titles

Full title

BMP-9 mediates fibroproliferation in fibrodysplasia ossificans progressiva through TGF-β signaling

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_doaj_primary_oai_doaj_org_article_738410d855c94041bf945288a48a8c04

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_738410d855c94041bf945288a48a8c04

Other Identifiers

ISSN

1757-4684,1757-4676

E-ISSN

1757-4684

DOI

10.1038/s44321-024-00174-3

How to access this item