Small fiber involvement is independent from clinical pain in late-onset Pompe disease
Small fiber involvement is independent from clinical pain in late-onset Pompe disease
About this item
Full title
Author / Creator
Enax-Krumova, Elena K. , Dahlhaus, Iris , Görlach, Jonas , Claeys, Kristl G. , Montagnese, Federica , Schneider, llka , Sturm, Dietrich , Fangerau, Tanja , Schlierbach, Hannah , Roth, Angela , Wanschitz, Julia V. , Löscher, Wolfgang N. , Güttsches, Anne-Katrin , Vielhaber, Stefan , Hasseli, Rebecca , Zunk, Lea , Krämer, Heidrun H. , Hahn, Andreas , Schoser, Benedikt , Rosenbohm, Angela and Schänzer, Anne
Publisher
England: BioMed Central Ltd
Journal title
Language
English
Formats
Publication information
Publisher
England: BioMed Central Ltd
Subjects
More information
Scope and Contents
Contents
Pain occurs in the majority of patients with late onset Pompe disease (LOPD) and is associated with a reduced quality of life. The aim of this study was to analyse the pain characteristics and its relation to a small nerve fiber involvement in LOPD patients.
In 35 patients with LOPD under enzyme replacement therapy without clinical signs of poly...
Alternative Titles
Full title
Small fiber involvement is independent from clinical pain in late-onset Pompe disease
Authors, Artists and Contributors
Author / Creator
Dahlhaus, Iris
Görlach, Jonas
Claeys, Kristl G.
Montagnese, Federica
Schneider, llka
Sturm, Dietrich
Fangerau, Tanja
Schlierbach, Hannah
Roth, Angela
Wanschitz, Julia V.
Löscher, Wolfgang N.
Güttsches, Anne-Katrin
Vielhaber, Stefan
Hasseli, Rebecca
Zunk, Lea
Krämer, Heidrun H.
Hahn, Andreas
Schoser, Benedikt
Rosenbohm, Angela
Schänzer, Anne
Identifiers
Primary Identifiers
Record Identifier
TN_cdi_doaj_primary_oai_doaj_org_article_8d4137d23d2245da8ad038e850fd7d75
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_doaj_primary_oai_doaj_org_article_8d4137d23d2245da8ad038e850fd7d75
Other Identifiers
ISSN
1750-1172
E-ISSN
1750-1172
DOI
10.1186/s13023-022-02327-4