Long-term kidney and liver outcome in 50 children with autosomal recessive polycystic kidney disease
Long-term kidney and liver outcome in 50 children with autosomal recessive polycystic kidney disease
About this item
Full title
Author / Creator
Dorval, Guillaume , Boyer, Olivia , Couderc, Anne , Delbet, Jean-Daniel , Heidet, Laurence , Debray, Dominique , Krug, Pauline , Girard, Muriel , Llanas, Brigitte , Charbit, Marina , Krid, Saoussen , Biebuyck, Nathalie , Fila, Marc , Courivaud, Cécile , Tilley, Frances , Garcelon, Nicolas , Blanc, Thomas , Chardot, Christophe , Salomon, Rémi and Lacaille, Florence
Publisher
Berlin/Heidelberg: Springer Berlin Heidelberg
Journal title
Language
English
Formats
Publication information
Publisher
Berlin/Heidelberg: Springer Berlin Heidelberg
Subjects
More information
Scope and Contents
Contents
Background
Autosomal recessive polycystic kidney disease (ARPKD) is a rare ciliopathy characterized by congenital hepatic fibrosis and cystic kidney disease. Lack of data about long-term follow-up makes it difficult to discuss timing and type of organ transplantation. Our objectives were to evaluate long-term evolution and indications for transp...
Alternative Titles
Full title
Long-term kidney and liver outcome in 50 children with autosomal recessive polycystic kidney disease
Authors, Artists and Contributors
Author / Creator
Boyer, Olivia
Couderc, Anne
Delbet, Jean-Daniel
Heidet, Laurence
Debray, Dominique
Krug, Pauline
Girard, Muriel
Llanas, Brigitte
Charbit, Marina
Krid, Saoussen
Biebuyck, Nathalie
Fila, Marc
Courivaud, Cécile
Tilley, Frances
Garcelon, Nicolas
Blanc, Thomas
Chardot, Christophe
Salomon, Rémi
Lacaille, Florence
Identifiers
Primary Identifiers
Record Identifier
TN_cdi_hal_primary_oai_HAL_hal_03967490v1
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_hal_primary_oai_HAL_hal_03967490v1
Other Identifiers
ISSN
0931-041X
E-ISSN
1432-198X
DOI
10.1007/s00467-020-04808-9