Clinical characteristics, functional respiratory decline and follow-up in adult patients with primar...
Clinical characteristics, functional respiratory decline and follow-up in adult patients with primary ciliary dyskinesia
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Publisher
England: BMJ Publishing Group LTD
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Language
English
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Publisher
England: BMJ Publishing Group LTD
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IntroductionPrimary ciliary dyskinesia (PCD) is a genetic disease characterised by abnormalities in ciliary function, responsible for chronic pulmonary and sinonasal diseases. Adult clinical features and outcome are poorly described.ObjectivesTo assess the clinical characteristics and disease progression in adults with PCD.MethodsBicentric retrospe...
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Clinical characteristics, functional respiratory decline and follow-up in adult patients with primary ciliary dyskinesia
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TN_cdi_hal_primary_oai_HAL_inserm_03875594v1
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https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_hal_primary_oai_HAL_inserm_03875594v1
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ISSN
0040-6376
E-ISSN
1468-3296
DOI
10.1136/thoraxjnl-2015-207891