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Effects of Home Mechanical Ventilation on Left Ventricular Function in Sarcoglycanopathies (Limb Gir...

Effects of Home Mechanical Ventilation on Left Ventricular Function in Sarcoglycanopathies (Limb Gir...

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_hal_primary_oai_HAL_inserm_04015389v1

Effects of Home Mechanical Ventilation on Left Ventricular Function in Sarcoglycanopathies (Limb Girdle Muscular Dystrophies)

About this item

Full title

Effects of Home Mechanical Ventilation on Left Ventricular Function in Sarcoglycanopathies (Limb Girdle Muscular Dystrophies)

Publisher

United States: Elsevier Inc

Journal title

The American journal of cardiology, 2018-07, Vol.122 (2), p.353-355

Language

English

Formats

Publication information

Publisher

United States: Elsevier Inc

More information

Scope and Contents

Contents

Cardiac and respiratory function may be impaired in sarcoglycanopathies, a subgroup of muscular dystrophies due to sarcoglycan proteins (α, β, γ, and δ) genes mutations. Management of patients with restrictive respiratory failure mainly relies on home mechanical ventilation (HMV). Little is known about the cardiac effects of prolonged mechanical ve...

Alternative Titles

Full title

Effects of Home Mechanical Ventilation on Left Ventricular Function in Sarcoglycanopathies (Limb Girdle Muscular Dystrophies)

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_hal_primary_oai_HAL_inserm_04015389v1

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_hal_primary_oai_HAL_inserm_04015389v1

Other Identifiers

ISSN

0002-9149

E-ISSN

1879-1913

DOI

10.1016/j.amjcard.2018.04.001

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