Premature aortic smooth muscle cell differentiation contributes to matrix dysregulation in Marfan Sy...
Premature aortic smooth muscle cell differentiation contributes to matrix dysregulation in Marfan Syndrome
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Full title
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Publisher
United States: Public Library of Science
Journal title
Language
English
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Publisher
United States: Public Library of Science
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Scope and Contents
Contents
Thoracic aortic aneurysm and dissection are life-threatening complications of Marfan syndrome (MFS). Studies of human and mouse aortic samples from late stage MFS demonstrate increased TGF-β activation/signaling and diffuse matrix changes. However, the role of the aortic smooth muscle cell (SMC) phenotype in early aneurysm formation in MFS has yet...
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Full title
Premature aortic smooth muscle cell differentiation contributes to matrix dysregulation in Marfan Syndrome
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TN_cdi_plos_journals_1952054195
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_plos_journals_1952054195
Other Identifiers
ISSN
1932-6203
E-ISSN
1932-6203
DOI
10.1371/journal.pone.0186603
