Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann Pick Disease
Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann Pick Disease
About this item
Full title
Author / Creator
Department of Pediatric Pulmonology, Gazi University School of Medicine, Ankara, Turkey , Clinic of Pediatric Pulmonology, Dr. Sami Ulus Maternity and Children Research and Training Hospital, Ankara, Turkey , Department of Interventional Radiology, Gazi University School of Medicine, Ankara, Turkey , Onay, Zeynep Reyhan , Ramasli Gursoy, Tugba , Tana Aslan, Ayse , Sismanlar Eyuboglu, Tugba and Akkan, Koray
Publisher
Ankara: Aves Yayincilik Ltd. STI
Journal title
Language
Formats
Publication information
Publisher
Ankara: Aves Yayincilik Ltd. STI
Subjects
More information
Scope and Contents
Contents
Introduction: Niemann Pick Disease (NPD) is a rare autosomal recessive hereditary disease and it causes abnormal storage of sphingomyelin in the tissues of reticuloendothelial system. When sphingomyelin storage affects the pulmonary system; recurrent pneumonia, dyspnea, clubbing can occur in the patients. Hepatopulmonary syndrome (HPS) and pulmonar...
Alternative Titles
Full title
Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann Pick Disease
Authors, Artists and Contributors
Author / Creator
Clinic of Pediatric Pulmonology, Dr. Sami Ulus Maternity and Children Research and Training Hospital, Ankara, Turkey
Department of Interventional Radiology, Gazi University School of Medicine, Ankara, Turkey
Onay, Zeynep Reyhan
Ramasli Gursoy, Tugba
Tana Aslan, Ayse
Sismanlar Eyuboglu, Tugba
Akkan, Koray
Identifiers
Primary Identifiers
Record Identifier
TN_cdi_proquest_journals_2548719370
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_journals_2548719370
Other Identifiers
ISSN
2149-2530
E-ISSN
2149-2530,2979-9139
DOI
10.5152/TurkThoracJ.2019.373
