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Cardiac electrical abnormalities in a mouse model of left ventricular non-compaction cardiomyopathy

Cardiac electrical abnormalities in a mouse model of left ventricular non-compaction cardiomyopathy

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_journals_3131948701

Cardiac electrical abnormalities in a mouse model of left ventricular non-compaction cardiomyopathy

About this item

Full title

Cardiac electrical abnormalities in a mouse model of left ventricular non-compaction cardiomyopathy

Publisher

Cold Spring Harbor: Cold Spring Harbor Laboratory Press

Journal title

bioRxiv, 2024-11

Language

English

Formats

Publication information

Publisher

Cold Spring Harbor: Cold Spring Harbor Laboratory Press

More information

Scope and Contents

Contents

Mutations in MINDBOMB 1 (MIB1), encoding an E3 ubiquitin ligase of the NOTCH signaling pathway, cause left ventricular noncompaction cardiomyopathy (LVNC) in mice and humans, increasing the risk of arrhythmia and left ventricular dysfunction. This study aimed to investigate the effect of MIB1 mutations on cardiac electrical activity. We examined ma...

Alternative Titles

Full title

Cardiac electrical abnormalities in a mouse model of left ventricular non-compaction cardiomyopathy

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_proquest_journals_3131948701

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_journals_3131948701

Other Identifiers

E-ISSN

2692-8205

DOI

10.1101/2024.11.20.624427