Mucopolysaccharide diseases: A complex interplay between neuroinflammation, microglial activation an...
Mucopolysaccharide diseases: A complex interplay between neuroinflammation, microglial activation and adaptive immunity
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Dordrecht: Springer Netherlands
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Language
English
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Dordrecht: Springer Netherlands
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Contents
Mucopolysaccharide (MPS) diseases are lysosomal storage disorders (LSDs) caused by deficiencies in enzymes required for glycosaminoglycan (GAG) catabolism. Mucopolysaccharidosis I (MPS I), MPS IIIA, MPS IIIB and MPS VII are deficient in the enzymes α–L-Iduronidase, Heparan-N-Sulphatase, N-Acetylglucosaminidase and Beta-Glucuronidase, respectively....
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Mucopolysaccharide diseases: A complex interplay between neuroinflammation, microglial activation and adaptive immunity
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TN_cdi_proquest_miscellaneous_1492621931
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_miscellaneous_1492621931
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ISSN
0141-8955
E-ISSN
1573-2665
DOI
10.1007/s10545-013-9613-3