The peroxisome deficient PEX2 Zellweger mouse: pathologic and biochemical correlates of lipid dysfun...
The peroxisome deficient PEX2 Zellweger mouse: pathologic and biochemical correlates of lipid dysfunction
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Author / Creator
Faust, P L , Su, H M , Moser, A and Moser, H W
Publisher
United States: Springer Nature B.V
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Language
English
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United States: Springer Nature B.V
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Contents
Zellweger syndrome is the prototypic human peroxisomal biogenesis disorder that results in abnormal neuronal migration in the central nervous system and severe neurologic dysfunction. A murine model for this disorder was previously developed by targeted deletion of the PEX2 peroxisomal gene. By labeling neuronal precursor cells in vivo with a mitot...
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The peroxisome deficient PEX2 Zellweger mouse: pathologic and biochemical correlates of lipid dysfunction
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TN_cdi_proquest_miscellaneous_71058244
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_miscellaneous_71058244
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ISSN
0895-8696
E-ISSN
0895-8696,1559-1166
DOI
10.1385/jmn:16:2-3:289