Log in to save to my catalogue

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_miscellaneous_858290096

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

About this item

Full title

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

Publisher

Berlin/Heidelberg: Springer-Verlag

Journal title

Pediatric nephrology (Berlin, West), 2011-03, Vol.26 (3), p.419-424

Language

English

Formats

Publication information

Publisher

Berlin/Heidelberg: Springer-Verlag

More information

Scope and Contents

Contents

The development of membranoproliferative glomerulonephritis (MPGN) is associated with uncontrolled activation of the complement alternative pathway. This dysregulation is related either to C3 nephritic factor (C3NeF), an auto-antibody directed against the alternative C3 convertase, or to homozygous loss-of-function mutation of the complement regula...

Alternative Titles

Full title

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_proquest_miscellaneous_858290096

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_proquest_miscellaneous_858290096

Other Identifiers

ISSN

0931-041X

E-ISSN

1432-198X

DOI

10.1007/s00467-010-1734-4

How to access this item