Oxidative stress in NPC1 deficient cells: protective effect of allopregnanolone
Oxidative stress in NPC1 deficient cells: protective effect of allopregnanolone
About this item
Full title
Author / Creator
Publisher
Oxford, UK: Blackwell Publishing Ltd
Journal title
Language
English
Formats
Publication information
Publisher
Oxford, UK: Blackwell Publishing Ltd
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More information
Scope and Contents
Contents
Niemann‐Pick C disease (NPC) is an autosomal recessive neurodegenerative disorder caused by the abnormal function of NPC1 or NPC2 proteins, leading to an accumulation of unesterified cholesterol and glycosphingolipids (GSLs) in the lysosomes. The mechanisms underlying the pathophysiology in NPC disease are not clear. Oxidative damage is implicated...
Alternative Titles
Full title
Oxidative stress in NPC1 deficient cells: protective effect of allopregnanolone
Authors, Artists and Contributors
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Primary Identifiers
Record Identifier
TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_2832077
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_2832077
Other Identifiers
ISSN
1582-1838
E-ISSN
1582-4934
DOI
10.1111/j.1582-4934.2008.00493.x
