Log in to save to my catalogue

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4299649

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

About this item

Full title

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

Publisher

United States: American Thoracic Society

Journal title

American journal of respiratory and critical care medicine, 2014-12, Vol.190 (12), p.1395-1401

Language

English

Formats

Publication information

Publisher

United States: American Thoracic Society

More information

Scope and Contents

Contents

The rate of progression of most interstitial lung diseases (ILD) is unpredictable. Fibrocytes are circulating bone marrow-derived cells that have been implicated in the pathogenesis of lung fibrosis. Hermansky-Pudlak syndrome (HPS), a genetic cause of ILD in early adulthood, allows for study of biomarkers of ILD in a homogeneous population at near-...

Alternative Titles

Full title

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4299649

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4299649

Other Identifiers

ISSN

1073-449X

E-ISSN

1535-4970

DOI

10.1164/rccm.201407-1287OC

How to access this item