Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences
Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences
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Publisher
Cairo, Egypt: Hindawi Publishing Corporation
Journal title
Language
English
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Publisher
Cairo, Egypt: Hindawi Publishing Corporation
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Scope and Contents
Contents
Cystic fibrosis (CF) is caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. The resultant characteristic ion transport defect results in decreased mucociliary clearance, bacterial colonisation, and chronic neutrophil-dominated inflammation. Much knowledge surrounding the pathophysiology of the disease has bee...
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Full title
Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences
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Record Identifier
TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4908263
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4908263
Other Identifiers
ISSN
2314-6133
E-ISSN
2314-6141
DOI
10.1155/2016/5258727