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Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4908263

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences

About this item

Full title

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences

Publisher

Cairo, Egypt: Hindawi Publishing Corporation

Journal title

BioMed research international, 2016-01, Vol.2016 (2016), p.1-14

Language

English

Formats

Publication information

Publisher

Cairo, Egypt: Hindawi Publishing Corporation

More information

Scope and Contents

Contents

Cystic fibrosis (CF) is caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. The resultant characteristic ion transport defect results in decreased mucociliary clearance, bacterial colonisation, and chronic neutrophil-dominated inflammation. Much knowledge surrounding the pathophysiology of the disease has bee...

Alternative Titles

Full title

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences

Identifiers

Primary Identifiers

Record Identifier

TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4908263

Permalink

https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_4908263

Other Identifiers

ISSN

2314-6133

E-ISSN

2314-6141

DOI

10.1155/2016/5258727

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