Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway
Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway
About this item
Full title
Author / Creator
García-Laorden, M. Isabel , Hernández-Brito, Elisa , Muñoz-Almagro, Carmen , Pavlovic-Nesic, Svetlana , Rúa-Figueroa, Iñigo , Briones, M. Luisa , Rajas, Olga , Borderías, Luis , Payeras, Antoni , Lorente, Leonardo , Freixinet, Jordi , Ferreres, Jose , Obando, Ignacio , González-Quevedo, Nereida , Rodríguez de Castro, Felipe , Solé-Violán, Jordi and Rodríguez-Gallego, Carlos
Publisher
New York: Springer US
Journal title
Language
English
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Publication information
Publisher
New York: Springer US
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More information
Scope and Contents
Contents
Mannose-binding lectin (MBL)-associated serine protease-2 (MASP-2) is an indispensable enzyme for the activation of the lectin pathway of complement. Its deficiency is classified as a primary immunodeficiency associated to pyogenic bacterial infections, inflammatory lung disease, and autoimmunity. In Europeans, MASP-2 deficiency, due to homozygosit...
Alternative Titles
Full title
Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway
Authors, Artists and Contributors
Author / Creator
Hernández-Brito, Elisa
Muñoz-Almagro, Carmen
Pavlovic-Nesic, Svetlana
Rúa-Figueroa, Iñigo
Briones, M. Luisa
Rajas, Olga
Borderías, Luis
Payeras, Antoni
Lorente, Leonardo
Freixinet, Jordi
Ferreres, Jose
Obando, Ignacio
González-Quevedo, Nereida
Rodríguez de Castro, Felipe
Solé-Violán, Jordi
Rodríguez-Gallego, Carlos
Identifiers
Primary Identifiers
Record Identifier
TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_7223972
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_7223972
Other Identifiers
ISSN
0271-9142
E-ISSN
1573-2592
DOI
10.1007/s10875-019-00714-4
