Immune-mediated myogenesis and acetylcholine receptor clustering promote a slow disease progression...
Immune-mediated myogenesis and acetylcholine receptor clustering promote a slow disease progression in ALS mouse models
About this item
Full title
Author / Creator
Margotta, Cassandra , Fabbrizio, Paola , Ceccanti, Marco , Cambieri, Chiara , Ruffolo, Gabriele , D'Agostino, Jessica , Trolese, Maria Chiara , Cifelli, Pierangelo , Alfano, Veronica , Laurini, Christian , Scaricamazza, Silvia , Ferri, Alberto , Sorarù, Gianni , Palma, Eleonora , Inghilleri, Maurizio , Bendotti, Caterina and Nardo, Giovanni
Publisher
England: Springer
Journal title
Language
English
Formats
Publication information
Publisher
England: Springer
Subjects
More information
Scope and Contents
Contents
Amyotrophic lateral sclerosis (ALS) is a heterogeneous disease in terms of onset and progression rate. This may account for therapeutic clinical trial failure. Transgenic SOD1G93A mice on C57 or 129Sv background have a slow and fast disease progression rate, mimicking the variability observed in patients. Based on evidence inferring the active infl...
Alternative Titles
Full title
Immune-mediated myogenesis and acetylcholine receptor clustering promote a slow disease progression in ALS mouse models
Authors, Artists and Contributors
Author / Creator
Fabbrizio, Paola
Ceccanti, Marco
Cambieri, Chiara
Ruffolo, Gabriele
D'Agostino, Jessica
Trolese, Maria Chiara
Cifelli, Pierangelo
Alfano, Veronica
Laurini, Christian
Scaricamazza, Silvia
Ferri, Alberto
Sorarù, Gianni
Palma, Eleonora
Inghilleri, Maurizio
Bendotti, Caterina
Nardo, Giovanni
Identifiers
Primary Identifiers
Record Identifier
TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_9996869
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_9996869
Other Identifiers
ISSN
1880-9693
E-ISSN
1880-8190
DOI
10.1186/s41232-023-00270-w