Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia
Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia
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Publisher
United States: American Thoracic Society
Journal title
Language
English
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Publisher
United States: American Thoracic Society
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Scope and Contents
Contents
The molecular mechanisms underlying Hermansky-Pudlak syndrome-associated interstitial pneumonia (HPSIP) are poorly understood but, as in idiopathic pulmonary fibrosis, may be linked to chronic alveolar epithelial type II cell (AECII) injury.
We studied the development of fibrosis and the role of AECII injury in various murine models of HPS.
H...
Alternative Titles
Full title
Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia
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TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_2913235
Permalink
https://devfeature-collection.sl.nsw.gov.au/record/TN_cdi_pubmedcentral_primary_oai_pubmedcentral_nih_gov_2913235
Other Identifiers
ISSN
1073-449X
E-ISSN
1535-4970
DOI
10.1164/rccm.200909-1414OC
