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Select record 21
ArticlesPeer ReviewedFull Text
Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation
Author / Creator:Accurso, Frank J ; Rowe, Steven M ; Clancy, J.P ; Boyle, Michael P ; Dunitz, Jordan M ; Durie, Peter R ; Sagel, Scott D ; Hornick, Douglas B ; Konstan, Michael W ; Donaldson, Scott H ; Moss, Richard B ; Pilewski, Joseph M ; Rubenstein, Ronald C ; Uluer, Ahmet Z ; Aitken, Moira L ; Freedman, Steven D ; Rose, Lynn M ; Mayer-Hamblett, Nicole ; Dong, Qunming ; Zha, Jiuhong ; Stone, Anne J ; Olson, Eric R ; Ordoñez, Claudia L ; Campbell, Preston W ; Ashlock, Melissa A ; Ramsey, Bonnie W
Publisher:Waltham, MA: Massachusetts Medical Society
Journal title:The New England journal of medicine, 2010-11, Vol.363 (21), p.1991-2003
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Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): a randomised, double-blind, placebo-controlled trial
Author / Creator:Wong, Conroy, Dr ; Jayaram, Lata, FRACP ; Karalus, Noel, FRACP ; Eaton, Tam, FRACP ; Tong, Cecilia, RN ; Hockey, Hans, MSc ; Milne, David, FRANZCR ; Fergusson, Wendy, BHSc ; Tuffery, Christine, BN ; Sexton, Paul, FRACP ; Storey, Louanne, BSc ; Ashton, Toni, Prof
Publisher:Kidlington: Elsevier Ltd
Journal title:The Lancet (British edition), 2012-08, Vol.380 (9842), p.660-667
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ArticlesPeer ReviewedFull Text
Enzyme-Replacement Therapy in Life-Threatening Hypophosphatasia
Author / Creator:Whyte, Michael P ; Greenberg, Cheryl R ; Salman, Nada J ; Bober, Michael B ; McAlister, William H ; Wenkert, Deborah ; Van Sickle, Bradley J ; Simmons, Jill H ; Edgar, Terence S ; Bauer, Martin L ; Hamdan, Mohamed A ; Bishop, Nick ; Lutz, Richard E ; McGinn, Mairead ; Craig, Stanley ; Moore, Jean N ; Taylor, John W ; Cleveland, Robert H ; Cranley, William R ; Lim, Ruth ; Thacher, Tom D ; Mayhew, Jill E ; Downs, Matthew ; Millán, José Luis ; Skrinar, Alison M ; Crine, Philippe ; Landy, Hal
Publisher:Waltham, MA: Massachusetts Medical Society
Journal title:The New England journal of medicine, 2012-03, Vol.366 (10), p.904-913
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ArticlesPeer ReviewedFull Text
Non–Cystic Fibrosis Bronchiectasis
Author / Creator:McShane, Pamela J. ; Naureckas, Edward T. ; Tino, Gregory ; Strek, Mary E.
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2013-09, Vol.188 (6), p.647-656
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ArticlesPeer ReviewedFull Text
Magnetic Resonance Imaging Detects Changes in Structure and Perfusion, and Response to Therapy in Early Cystic Fibrosis Lung Disease
Author / Creator:Wielpütz, Mark O. ; Puderbach, Michael ; Kopp-Schneider, Annette ; Stahl, Mirjam ; Fritzsching, Eva ; Sommerburg, Olaf ; Ley, Sebastian ; Sumkauskaite, Migle ; Biederer, Jürgen ; Kauczor, Hans-Ulrich ; Eichinger, Monika ; Mall, Marcus A.
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2014-04, Vol.189 (8), p.956-965
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ArticlesPeer ReviewedFull Text
Clinical Care Guidelines for Cystic Fibrosis-Related Diabetes: A position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed b...
Author / Creator:MORAN, Antoinette ; BRUNZELL, Carol ; COHEN, Richard C ; KATZ, Marcia ; MARSHALL, Bruce C ; ONADY, Gary ; ROBINSON, Karen A ; SABADOSA, Kathryn A ; STECENKO, Arlene ; SLOVIS, Bonnie
Publisher:Alexandria, VA: American Diabetes Association
Journal title:Diabetes care, 2010-12, Vol.33 (12), p.2697-2708
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Cystic fibrosis
Author / Creator:O'Sullivan, Brian P, Prof ; Freedman, Steven D, MD
Publisher:Kidlington: Elsevier Ltd
Journal title:The Lancet (British edition), 2009-05, Vol.373 (9678), p.1891-1904
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Progression of early structural lung disease in young children with cystic fibrosis assessed using CT
Author / Creator:Mott, Lauren S ; Park, Judy ; Murray, Conor P ; Gangell, Catherine L ; de Klerk, Nicholas H ; Robinson, Philip J ; Robertson, Colin F ; Ranganathan, Sarath C ; Sly, Peter D ; Stick, Stephen M
Publisher:London: BMJ Publishing Group
Journal title:Thorax, 2012-06, Vol.67 (6), p.509-516
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ArticlesPeer ReviewedFull Text
Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality
Author / Creator:Moran, Antoinette ; Dunitz, Jordan ; Nathan, Brandon ; Saeed, Asad ; Holme, Bonnie ; Thomas, William
Publisher:Alexandria, VA: American Diabetes Association
Journal title:Diabetes care, 2009-09, Vol.32 (9), p.1626-1631
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ArticlesPeer ReviewedFull Text
Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs
Author / Creator:Rogers, Christopher S ; Stoltz, David A ; Meyerholz, David K ; Ostedgaard, Lynda S ; Rokhlina, Tatiana ; Taft, Peter J ; Rogan, Mark P ; Pezzulo, Alejandro A ; Karp, Philip H ; Itani, Omar A ; Kabel, Amanda C ; Wohlford-Lenane, Christine L ; Davis, Greg J ; Hanfland, Robert A ; Smith, Tony L ; Samuel, Melissa ; Wax, David ; Murphy, Clifton N ; Rieke, August ; Whitworth, Kristin ; Uc, Aliye ; Starner, Timothy D ; Brogden, Kim A ; Shilyansky, Joel ; McCray, Paul B. Jr ; Zabner, Joseph ; Prather, Randall S ; Welsh, Michael J
Publisher:Washington, DC: American Association for the Advancement of Science
Journal title:Science (American Association for the Advancement of Science), 2008-09, Vol.321 (5897), p.1837-1841
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Select record 31
ArticlesPeer ReviewedFull Text
A Functional Anatomic Defect of the Cystic Fibrosis Airway
Author / Creator:Birket, Susan E. ; Chu, Kengyeh K. ; Liu, Linbo ; Houser, Grace H. ; Diephuis, Bradford J. ; Wilsterman, Eric J. ; Dierksen, Gregory ; Mazur, Marina ; Shastry, Suresh ; Li, Yao ; Watson, John D. ; Smith, Alexander T. ; Schuster, Benjamin S. ; Hanes, Justin ; Grizzle, William E. ; Sorscher, Eric J. ; Tearney, Guillermo J. ; Rowe, Steven M.
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2014-08, Vol.190 (4), p.421-432
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Select record 32
ArticlesPeer ReviewedFull Text
The primary hyperoxalurias
Author / Creator:Hoppe, Bernd ; Beck, Bodo B. ; Milliner, Dawn S.
Publisher:Basingstoke: Elsevier Inc
Journal title:Kidney international, 2009-06, Vol.75 (12), p.1264-1271
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ArticlesPeer ReviewedFull Text
Hyperoxaluria: a gut–kidney axis?
Author / Creator:Robijn, Stef ; Hoppe, Bernd ; Vervaet, Benjamin A. ; D'Haese, Patrick C. ; Verhulst, Anja
Publisher:Basingstoke: Elsevier Inc
Journal title:Kidney international, 2011-12, Vol.80 (11), p.1146-1158
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Select record 34
ArticlesPeer ReviewedFull Text
Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis
Author / Creator:Quinton, Paul M, Prof
Publisher:London: Elsevier Ltd
Journal title:The Lancet (British edition), 2008-08, Vol.372 (9636), p.415-417
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Select record 35
ArticlesPeer ReviewedFull Text
Lung Clearance Index as an Outcome Measure for Clinical Trials in Young Children with Cystic Fibrosis. A Pilot Study Using Inhaled Hypertonic Saline
Author / Creator:Subbarao, Padmaja ; Stanojevic, Sanja ; Brown, Meghan ; Jensen, Renee ; Rosenfeld, Margaret ; Davis, Stephanie ; Brumback, Lyndia ; Gustafsson, Per ; Ratjen, Felix
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2013-08, Vol.188 (4), p.456-460
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Select record 36
ArticlesPeer ReviewedFull Text
Exacerbation frequency and clinical outcomes in adult patients with cystic fibrosis
Author / Creator:de Boer, Kaïssa ; Vandemheen, Katherine L ; Tullis, Elizabeth ; Doucette, Steve ; Fergusson, Dean ; Freitag, Andreas ; Paterson, Nigel ; Jackson, Mary ; Lougheed, M Diane ; Kumar, Vijay ; Aaron, Shawn D
Publisher:London: BMJ Publishing Group Ltd and British Thoracic Society
Journal title:Thorax, 2011-08, Vol.66 (8), p.680-685
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Select record 37
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Genetic Modifiers of Cystic Fibrosis–Related Diabetes
Author / Creator:Blackman, Scott M. ; Commander, Clayton W. ; Watson, Christopher ; Arcara, Kristin M. ; Strug, Lisa J. ; Stonebraker, Jaclyn R. ; Wright, Fred A. ; Rommens, Johanna M. ; Sun, Lei ; Pace, Rhonda G. ; Norris, Sarah A. ; Durie, Peter R. ; Drumm, Mitchell L. ; Knowles, Michael R. ; Cutting, Garry R.
Publisher:Alexandria, VA: American Diabetes Association
Journal title:Diabetes (New York, N.Y.), 2013-10, Vol.62 (10), p.3627-3635
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Select record 38
ArticlesPeer ReviewedFull Text
A Th17- and Th2-skewed Cytokine Profile in Cystic Fibrosis Lungs Represents a Potential Risk Factor for Pseudomonas aeruginosa Infection
Author / Creator:Tiringer, Kerstin ; Treis, Angela ; Fucik, Petra ; Gona, Mia ; Gruber, Saskia ; Renner, Sabine ; Dehlink, Eleonora ; Nachbaur, Edith ; Horak, Friedrich ; Jaksch, Peter ; Döring, Gerd ; Crameri, Reto ; Jung, Andreas ; Rochat, Mascha K. ; Hörmann, Marcus ; Spittler, Andreas ; Klepetko, Walter ; Akdis, Cezmi A. ; Szépfalusi, Zsolt ; Frischer, Thomas ; Eiwegger, Thomas
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2013-03, Vol.187 (6), p.621-629
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Select record 39
ArticlesPeer ReviewedFull Text
Monitoring Cystic Fibrosis Lung Disease by Computed Tomography. Radiation Risk in Perspective
Author / Creator:Kuo, Wieying ; Ciet, Pierluigi ; Tiddens, Harm A. W. M. ; Zhang, Wei ; Guillerman, R. Paul ; van Straten, Marcel
Publisher:New York, NY: American Thoracic Society
Journal title:American journal of respiratory and critical care medicine, 2014-06, Vol.189 (11), p.1328-1336
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Select record 40
ArticlesPeer ReviewedFull Text
Effect of Estrogen on Pseudomonas Mucoidy and Exacerbations in Cystic Fibrosis
Author / Creator:Chotirmall, Sanjay H ; Smith, Stephen G ; Gunaratnam, Cedric ; Cosgrove, Sonya ; Dimitrov, Borislav D ; O'Neill, Shane J ; Harvey, Brian J ; Greene, Catherine M ; McElvaney, Noel G
Publisher:Waltham, MA: Massachusetts Medical Society
Journal title:The New England journal of medicine, 2012-05, Vol.366 (21), p.1978-1986
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Showing 21 to 40 of 1,052 results

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Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation

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Azithromycin for prevention of exacerbations in non-cystic fibrosis bronchiectasis (EMBRACE): a randomised, double-blind, placebo-controlled trial

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Enzyme-Replacement Therapy in Life-Threatening Hypophosphatasia

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Non–Cystic Fibrosis Bronchiectasis

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Magnetic Resonance Imaging Detects Changes in Structure and Perfusion, and Response to Therapy in Early Cystic Fibrosis Lung Disease

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Clinical Care Guidelines for Cystic Fibrosis-Related Diabetes: A position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed b...

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Cystic fibrosis

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Progression of early structural lung disease in young children with cystic fibrosis assessed using CT

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Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality

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Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs

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A Functional Anatomic Defect of the Cystic Fibrosis Airway

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The primary hyperoxalurias

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Hyperoxaluria: a gut–kidney axis?

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Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

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Lung Clearance Index as an Outcome Measure for Clinical Trials in Young Children with Cystic Fibrosis. A Pilot Study Using Inhaled Hypertonic Saline

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Exacerbation frequency and clinical outcomes in adult patients with cystic fibrosis

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Genetic Modifiers of Cystic Fibrosis–Related Diabetes

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A Th17- and Th2-skewed Cytokine Profile in Cystic Fibrosis Lungs Represents a Potential Risk Factor for Pseudomonas aeruginosa Infection

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Monitoring Cystic Fibrosis Lung Disease by Computed Tomography. Radiation Risk in Perspective

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Effect of Estrogen on Pseudomonas Mucoidy and Exacerbations in Cystic Fibrosis

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